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Rhomboid fossa

The rhomboid fossa, also known as the floor of the , is a diamond-shaped depression in the posterior aspect of the formed by the dorsal surfaces of the and the open portion of the . It serves as the ventral wall of the , a cerebrospinal fluid-filled in the , and is lined by ependymal cells. This structure is critical in due to its role in housing several cranial nerve nuclei and providing a landmark for organization. The rhomboid fossa exhibits a symmetrical, rhomboidal outline, typically measuring approximately 2-3 cm in length and 1-2 cm in width, with its superior apex at the and inferior apex near the of the . It is divided into three main parts: an upper triangular portion corresponding to the , an intermediate rhomboidal section, and a lower triangular area from the medulla. A prominent median sulcus runs longitudinally down its center, dividing it into left and right halves and featuring the , which includes elevations such as the (formed by the genu of the looping over the ) and the hypoglossal and vagal trigones. Lateral to the sulcus limitans, the vestibular area contains nuclei associated with balance and eye movements. Transverse striae medullares, strands of fibers from the arcuate nuclei, cross the upper part of the fossa, distinguishing the pontine from the medullary regions and contributing to cerebellar connections via the arcuatocerebellar tract. The , a cluster of noradrenergic neurons, is located in the lateral floor of the rhomboid fossa, playing a key role in and responses. Embryologically, the rhomboid fossa develops from the dorsal wall of the in the and during the fifth week of , thinning to form the ventricular floor as the segments. Its anatomical landmarks are essential for surgical approaches in procedures, guiding safe entry zones while avoiding critical nuclei and tracts.

Overview

Definition

The rhomboid fossa is a diamond- or rhombus-shaped depression that forms the floor of the fourth ventricle, a cerebrospinal fluid-filled cavity in the hindbrain. This structure lies on the dorsal surfaces of the pons and medulla oblongata, providing a key anatomical landmark in the brainstem. In adults, the rhomboid fossa measures approximately 3.5 cm in length and 2.3 cm in width, though these dimensions can vary slightly between individuals. The term "rhomboid" derives from the Greek rhombos, referring to its rhombus-like geometric form, while "fossa" comes from the Latin word for a trench or depression, aptly describing its shallow, pitted appearance. The rhomboid fossa consists primarily of a thin layer of gray matter, continuous with that of the and underlying the nuclei of several , and is covered by a delicate that lines the . This facilitates the circulation of within the .

Location and relations

The rhomboid fossa is situated in the posterior aspect of the and the open , forming the floor of the . It appears as a diamond-shaped depression on the dorsal surface of these brainstem structures, extending superiorly from the to the inferiorly. This positioning places the fossa centrally within the , contributing to the ventricular system's architecture for circulation. The rhomboid fossa features the sulcus limitans laterally, a longitudinal groove that separates the medial eminence—containing motor nuclei—from the adjacent vestibular and cochlear areas overlying sensory nuclei. The sulcus limitans runs parallel to the median sulcus along the length of the fossa, delineating these functional zones. Superiorly, the rhomboid fossa is continuous with the , providing a conduit for from the third ventricle. Inferiorly, it transitions at the into the of the , marking the caudal limit of the . Surrounding structures include the roof of the , formed by the superior and inferior medullary vela attached to the and incorporating for production; anteriorly, the fossa relates to the via the ventral tissue.

Anatomy

Overall structure

The rhomboid fossa constitutes the diamond-shaped floor of the , formed by the dorsal surfaces of the and the open portion of the . It exhibits a division along its rostrocaudal extent, comprising a superior part corresponding to the pontine recess, an part in the medullary portion, and an inferior part forming the closed medulla triangle. This arrangement reflects the underlying segmentation, with the superior part being triangular and positioned rostrally, the part representing the broadest central region, and the inferior part tapering to a caudal apex. The central axis of the rhomboid fossa aligns along the midline, facilitating symmetrical neural organization, while lateral expansions occur at the recesses to accommodate adjacent structures such as the cerebellar peduncles. Its surface appearance features a relatively smooth central area interspersed with elevated regions, including trigones and colliculi, which contribute to the fossa's characteristic rhomboidal contour. As the floor of the , it provides a critical interface for circulation and houses key nuclei. Vascular supply to the rhomboid fossa derives primarily from the vertebrobasilar system, with branches from the (PICA) perfusing the lateral aspects of the medullary components and the providing medial supply to the inferior regions. In the pontine portion, additional contributions come from paramedian branches of the and circumferential branches of the , ensuring robust oxygenation to the underlying neural tissue. These arterial distributions are essential for maintaining the metabolic demands of the densely packed nuclei and tracts within the fossa.

Parts and boundaries

The rhomboid fossa is divided into three distinct parts: superior, intermediate, and inferior, forming its characteristic diamond-shaped floor within the . The superior part is triangular in shape, extending from the opening of the superiorly to the level of the pontine flexure inferiorly, and is bounded laterally by the superior cerebellar peduncles. This region, formed by the dorsal surface of the , measures approximately 1 cm in length. The intermediate part assumes a rhomboidal configuration, spanning the area between the pontomedullary junction superiorly and the inferiorly, and features lateral recesses that open into the foramina of Luschka. It is limited laterally by the middle cerebellar peduncles and measures about 1.5 cm in length. The inferior part is a triangular area known as the calamus scriptorius, with its base adjacent to the and apex directed downward into the of the , measuring roughly 0.5 cm in length. Overall, the rhomboid fossa is bounded superiorly by the , inferiorly by the , laterally by the foramina of Luschka within the lateral recesses, and centrally by the medial eminence flanking the median sulcus.

Floor features

The floor of the rhomboid fossa, forming the posterior surface of the and upper , presents a series of distinct elevations, depressions, and grooves that serve as surface landmarks for underlying neural structures. These features are divided by the median sulcus into symmetrical halves, with the sulcus limitans running laterally to separate motor and sensory regions. The appears as an oval elevation in the pontine portion of the floor, situated in the medial eminence opposite the superior fovea. It is formed by the motor fibers of the (cranial nerve VII) looping dorsally around the abducent nucleus (cranial nerve ) before descending to exit the . This prominence lies within the superior part of the rhomboid fossa, providing a key rostral landmark. In the medullary portion, the hypoglossal trigone manifests as a longitudinal elevation medial to the sulcus limitans, overlying the hypoglossal nucleus. Adjacent and lateral to it lies the vagal trigone, a triangular depression or elevation that covers the dorsal motor nucleus of the . The vagal trigone, also known as the ala cinerea, extends from the calamus scriptorius at its base to an apex near the acoustic striae, with its medial third housing the dorsal motor nucleus and the lateral two-thirds the nucleus of the solitary tract. At the caudal tip of the rhomboid fossa, near the , the emerges as a paired, highly vascularized prominence bounded superiorly by the funiculus separans and inferiorly by the gracile . This structure, composed of ependymal cells, glia, neurons, and fenestrated capillaries, lacks a typical blood-brain barrier, functioning as a . The sulcus limitans constitutes a shallow longitudinal groove along the lateral margin of the medial eminence, delineating the boundary between motor (medial) and sensory (lateral) domains of the floor. It widens superiorly into the superior fovea, a small at the level of the , and inferiorly into the inferior fovea, a depression marking the transition to the medullary region. These foveae serve as subtle indentations highlighting the positions of underlying cranial nerve nuclei. Crossing the intermediate portion of the floor are the striae medullares, fine transverse bundles of arcuate fibers from the arcuate nuclei of the medulla oblongata that extend obliquely from the vestibular area toward the median sulcus. These strands divide the rhomboid fossa into upper and lower triangles, contributing to its characteristic diamond shape.

Histology

Epithelial covering

The rhomboid fossa, forming the floor of the fourth ventricle, is lined by a layer of ependymal cells that constitute a simple ciliated columnar epithelium derived from neuroepithelial precursors. These cells feature apical cilia and microvilli that facilitate the directional propulsion of cerebrospinal fluid (CSF) across the ventricular surface, aiding in its circulation within the central nervous system. The ependymal layer maintains a uniform, single-cell thickness typically ranging from 10 to 20 micrometers, providing a protective interface between the CSF and underlying neural tissue. In specialized regions such as the , located at the caudal aspect of the rhomboid fossa, the ependymal covering transitions to a thinner, modified form composed of flattened tanycyte-like cells with reduced ciliature. This region overlies fenestrated capillaries that enable direct exchange with the bloodstream, distinguishing it from the standard ependymal barrier. The ependyma of the rhomboid fossa is continuous with the epithelial lining of the adjacent , where similar ciliated cells contribute to CSF production and dynamics. The ependymal covering serves as a selective permeability barrier, forming tight junctions that regulate the passage of ions, nutrients, and metabolites between the CSF and parenchyma, thus contributing to the blood-CSF barrier. However, at circumventricular organs like the , this barrier is attenuated, permitting the detection of circulating hormones and toxins while restricting broader access through specialized tanycytic processes.

Underlying neural elements

The underlying neural elements of the rhomboid fossa consist primarily of the tegmental gray matter from the and upper , which forms the dorsal aspect of the and is rich in neuronal organized into various nuclei. This gray matter lies immediately beneath the ependymal lining and includes clusters of neurons that integrate sensory and motor functions essential to brainstem operations. Glial elements, including and , provide structural and metabolic support to this region, with contributing to the blood-brain barrier integrity around subependymal areas and facilitating myelination of adjacent tracts. These glial cells are particularly prominent in areas like the , where they form a specialized, highly vascular lacking a typical blood-brain barrier. Key nuclear groups embedded within the floor include the (superior, medial, lateral, and inferior), which occupy the vestibular area and process balance-related inputs; the cochlear nuclei ( and ventral), located at the pontomedullary junction and forming the acoustic ; and the nucleus of the solitary tract, which spans the medullary portion and handles visceral sensory afferents. These nuclei are situated deep to the , with their positions corresponding to surface landmarks such as the vestibular area and vagal trigone. Connectivity in this region involves fibers from several that either loop through or pierce the floor en route to their nuclei. For instance, (CN VII) fibers loop dorsally around the abducens nucleus within the before exiting; (CN VIII) afferents terminate directly in the vestibular and cochlear nuclei; glossopharyngeal (CN IX) and vagus (CN X) fibers project to the for sensory relay; and (CN XII) rootlets originate from the hypoglossal nucleus and course ventrally, piercing the medullary .

Development

Embryonic origins

The rhomboid fossa originates from the region of the embryonic , specifically within the rhombencephalon, which is transiently segmented into eight rhombomeres (r1 to r8). These rhombomeres represent compartmentalized units that establish the anteroposterior patterning of the , with the rhomboid fossa forming as the ventral midline floor of the emerging anlage. The dorsal closure of the in the region during the fourth week of sets the stage for this segmentation, where each rhombomere contributes to distinct neuronal populations underlying the fossa's future structures. The development of the rhomboid fossa's ventral midline is critically induced by signals from the and the floor plate of the . The , a midline mesodermal structure, secretes Sonic hedgehog (Shh) protein, which induces the overlying cells to differentiate into floor plate cells along the ventral midline of the rhombencephalon. These floor plate cells then amplify Shh signaling, creating a concentration gradient that patterns ventral cell fates, including the ependymal lining and associated nuclei that will form the rhomboid fossa. This inductive process ensures the precise dorsoventral organization essential for the fossa's diamond-shaped configuration. By the fifth week of (Carnegie stage 14), the rhomboid fossa becomes apparent as part of the fourth ventricle's anlage, coinciding with the initial expansion of the rhombencephalic cavity. At this stage, the fossa's outline emerges in the ventral wall of the developing ventricle, marking the early delineation of its boundaries within the and medulla precursors. Genetic regulation of the rhomboid fossa's origins involves Hox genes, which provide the combinatorial codes for rhombomere-specific identities in the rhombencephalon. , such as Hoxa1, Hoxb1, and members of the Hoxb cluster, are expressed in nested domains across r1 to r8, with specific combinations (e.g., Hoxb1 restricted to r4) directing segmental patterning and the positioning of ventral midline elements that contribute to the fossa. These genes integrate upstream signals like to refine rhombomere boundaries and ensure aligned neuronal differentiation along the future rhomboid fossa.

Formation and maturation

The formation of the rhomboid fossa begins during the early embryonic period as the undergoes significant flexures that expand the floor of the developing . During the fifth week of , the pontine flexure emerges at the level of the future , causing the to bend dorsally and "gape open" along its line of fusion, which directly contributes to the diamond-shaped contour of the rhomboid fossa. Concurrently, the medullary (or cervical) flexure at the junction of the and further widens the ventricular floor between weeks 6 and 8, establishing the foundational rhomboid morphology as the alar plates shift laterally relative to the basal plates. By approximately 12 weeks of gestation, the caudal end of the narrows at the , marking the transition to the of the and delineating the calamus scriptorius region of the rhomboid fossa. This process refines the fossae's boundaries, separating the open portion of the from the closed medullary segment and ensuring proper containment. Postnatally, the rhomboid fossa exhibits minimal structural growth, as its dimensions are largely established , but underlying neural maturation continues through myelination of tracts and nuclei. Myelination in the , including fibers adjacent to the fossae floor, progresses rapidly from late and reaches completion by approximately 2 years of age, enhancing signal conduction efficiency without altering the . Developmental anomalies, such as those seen in Chiari malformations, can disrupt this process by causing underdevelopment of the , leading to altered rhomboid fossa shape due to cerebellar tonsillar herniation that compresses the floor.

Function

Role in CSF circulation

The rhomboid fossa, forming the floor of the , plays a key role in directing (CSF) flow through the coordinated ciliary action of its ependymal lining. The , a specialized epithelial layer covering the fossa, features motile cilia that beat rhythmically to propel CSF entering from the toward the lateral apertures, known as the foramina of Luschka. This ciliary propulsion is essential for maintaining unidirectional flow within the narrow confines of the , ensuring efficient circulation without stagnation. The ependymal cilia, protruding from multiciliated cells, generate a metachronal wave that facilitates this transport, with beating frequencies typically ranging from 28 to 40 Hz in mammalian models. Integration with the further enhances the rhomboid fossa's contribution to CSF dynamics, particularly in the lateral recesses. The , a vascularized structure within these recesses, contributes to total CSF production, which occurs at a rate of approximately 0.3–0.4 mL/min in adults, with the accounting for about 10–20% of the total daily CSF volume. This newly formed CSF mixes with incoming fluid from the aqueduct and is directed by ependymal cilia toward the foramina of Luschka, where the plexus itself protrudes to facilitate direct release into the subarachnoid space. Such integration ensures a steady supply and distribution of CSF, supporting nutrient delivery and waste removal in the posterior fossa. The thin structure of the rhomboid fossa's floor also aids in pressure regulation by allowing transmission of subarachnoid space pressure changes to the ventricular interior. Composed of a delicate layer of neural tissue and , the fossa acts as a compliant barrier that equalizes hydrostatic pressures, preventing excessive ventricular dilation during fluctuations in . This mechanism is crucial for maintaining CSF , as it permits subtle adjustments in response to pulsatile arterial flows or postural changes. At its inferior apex, the marks the narrowing of the into the of the , directing the majority of CSF outward through the apertures while only a small amount enters the due to the and flow dynamics. This configuration helps sustain forward momentum in CSF circulation, reducing the risk of accumulation in the lower ventricular extensions.

Associated brainstem nuclei

The rhomboid fossa, forming the floor of the , harbors several key nuclei associated with cranial nerve functions, embedded within its pontine and medullary portions. These nuclei include both motor and sensory components that contribute to essential neural signaling pathways. In the pontine region, motor nuclei are prominently featured. The abducens nucleus (cranial nerve VI), located in the dorsal aspect of the caudal near the midline, underlies the and controls innervation for eye abduction. Adjacent to it, the facial motor nucleus (cranial nerve VII) resides deeper in the pontine , with its axons forming intra-axial loops that course dorsomedially over the abducens nucleus, elevating the overlying before exiting the . Shifting to the medullary segment, additional motor nuclei are situated within specialized trigones of the rhomboid fossa floor. The hypoglossal nucleus (cranial XII), positioned in the hypoglossal trigone medial to the vagal trigone, provides somatic motor innervation to the muscles. The dorsal motor nucleus of the vagus (cranial X), occupying the medial third of the vagal trigone (also known as the ala cinerea), serves as the primary parasympathetic outflow for visceral organs in the and . Sensory nuclei are also integral to the rhomboid fossa's structure. The (cranial nerve VIII), comprising superior, medial, lateral, and inferior components, lie within the vestibular area (area acustica) lateral to the sulcus limitans, processing balance and spatial orientation inputs from the . The nucleus of the solitary tract, receiving sensory afferents from IX and X, extends across the lateral two-thirds of the vagal trigone, handling visceral sensory information including and baroreception. A notable special feature is the , a noradrenergic appearing as a bluish-gray area above the superior fovea in the upper rhomboid fossa; it consists of pigmented neurons that modulate arousal, attention, and stress responses throughout the .

Clinical significance

Pathological conditions

The rhomboid fossa, forming the floor of the , can be distorted in Dandy-Walker malformation, a congenital anomaly characterized by cystic dilation of the due to failure of integration of the anterior membranous area in the plica choroidalis, leading to or of the and elevation of the tentorium cerebelli. This enlargement results in a large posterior cyst representing the dilated , which compresses and distorts the rhomboid fossa, often accompanied by in up to 80% of cases. Clinical manifestations include , developmental delay, and increased , with the distortion potentially impairing circulation at the ventricular outlets. Lesions involving the , a circumventricular located at the caudal end of the rhomboid fossa in the dorsal medulla, are implicated in various pathological states. In neuromyelitis optica spectrum disorders, often overlapping with , inflammatory plaques selectively target aquaporin-4 channels in the , causing tissue rarefaction, vascular thickening, and immune cell infiltration without significant neuronal loss. These lesions, observed in approximately 40% of cases, manifest as area postrema syndrome with intractable , , and hiccups, increasing the odds of these symptoms by 16-fold compared to unaffected patients. Additionally, the serves as the for emesis, where chemotherapy agents stimulate and serotonin receptors, inducing and through activation of the vomiting center in the medulla. Tumors originating from the ependymal lining of the rhomboid fossa, such as ependymomas and medulloblastomas, pose significant risks due to their location and potential for obstructive . Ependymomas, the third most common pediatric , frequently arise in the adjacent to the rhomboid fossa, exhibiting a nodular pattern with perivascular pseudorosettes and often infiltrating the floor, complicating surgical resection. Medulloblastomas, the most common malignant pediatric , can originate from embryonic cells in the inferior rhomboid fossa or external granular layer, with 45% of those arising from the showing infiltrative attachment to the caudal rhomboid fossa in surgical cases, leading to symptoms like , , and cerebellar dysfunction. These tumors may disseminate via pathways, necessitating multidisciplinary management. Inflammatory conditions like rhombencephalitis directly affect the rhomboid fossa by targeting embedded nuclei, resulting in cranial neuropathies. is the most common cause, leading to encephalitis with involvement of cranial nerve nuclei in the and medulla, commonly manifesting as ophthalmoplegia, facial weakness, and . The disrupts nuclear groups along the rhomboid fossa, such as the abducens and facial nuclei, causing a spectrum of deficits including and respiratory compromise. Autoimmune variants may similarly inflame these structures, exacerbating neuropathies through immune-mediated damage. Vascular pathologies, particularly infarcts in the (PICA) territory, underlie Wallenberg syndrome (), involving the rhomboid fossa-related sensory nuclei in the medulla. The infarct disrupts the and tract, as well as the nucleus of the solitary tract—both embedded in the floor of the —producing ipsilateral facial and contralateral body hypoalgesia due to deafferentation of second-order neurons. Additional features include Horner syndrome, , and vertigo from involvement of adjacent sympathetic fibers and , with the rhomboid fossa's superficial position rendering these nuclei vulnerable to ischemic insult. varies, but sensory deficits often persist, highlighting the critical role of these fossa-associated structures in sensory integration.

Diagnostic and surgical considerations

(MRI), particularly T2-weighted sequences, is essential for visualizing the rhomboid fossa, as it delineates the floor of the with high contrast, revealing abnormalities such as hyperintensities or flattening associated with underlying pathologies. T2-weighted MRI also aids in assessing lesions extending along the rhomboid fossa, facilitating preoperative planning without obstructing cerebrospinal fluid (CSF) flow visualization. Computed tomography (CT) cisternography complements MRI by evaluating CSF dynamics around the , identifying obstructions at the rhomboid fossa level through contrast-enhanced flow patterns. Endoscopic techniques provide direct intraventricular visualization of the rhomboid fossa during procedures for , such as third ventriculostomy or of Magendie opening, allowing assessment of floor integrity and outlet patency in cases of obstruction. Surgical access to the rhomboid fossa typically involves suboccipital for posterior fossa tumors, enabling telovelar or midline approaches while prioritizing preservation of the fossa's neural elements to minimize disruption. Intraoperative monitoring using cranial nerve evoked potentials, including corticobulbar motor evoked potentials, protects associated nuclei by detecting real-time functional changes during tumor resection near the floor. Rhomboid fossa involvement in tumors, such as ependymomas, serves as a prognostic factor, indicating elevated risk of persistent due to impaired CSF pathways, with incomplete resection further exacerbating postoperative complications.